cystic lymphangioma
Enable an agent to recognize a lesion recorded as cystic lymphangioma, characterize its extent and clinical state, and support evidence-based specialist assessment and follow-up.
Bundle → Layer → Finding → Questions Filled
6 bundles · 11 layers · 17 findings · 27 questions
Diagnostic identity Establish what the label cystic lymphangioma means in this case and which evidence supports that interpretation.
Terminology mapping
Preserve the original diagnosis alongside its proposed modern interpretation.
Historical label interpretation
Record who used the label, its clinical context, and whether a specialist has mapped it to a specific lymphatic-malformation category.
- Which report first called the lesion cystic lymphangioma, and what evidence accompanied that label? provenance
- Does the available evidence support a particular lymphatic-malformation subtype, or only an unspecified cystic lymphatic lesion? definition
Diagnostic support
Connect the interpretation to clinical, imaging, and any available pathological evidence.
Concordance and mimics
Record the location-specific differential, evidence favoring lymphatic origin, and unresolved discrepancies without making tissue sampling a universal requirement.
- Which examination, imaging, or existing pathology findings support lymphatic origin? provenance
- Which competing diagnosis remains plausible, and what discordant feature would require specialist reassessment? boundary
Cyst architecture and extent Describe the cystic lesion as a spatial structure with measurable components.
Cyst morphology
Characterize individual cysts and their contribution to the overall lesion.
Cyst pattern and measurement
Record representative cyst sizes, septations, contents, and the convention used to assign a morphology category.
- What are the measured cyst diameters and overall lesion dimensions, using which modality and date? measurement
- Which observed features justify macrocystic, microcystic, mixed, or indeterminate classification? definition
Anatomical relationships
Locate the lesion across tissue compartments and relative to structures that constrain management.
Extent and critical interfaces
Record mapped boundaries, uncertain extension, and compression or encasement of relevant structures.
- Which compartments are involved, and which lesion boundaries remain incompletely visualized? measurement
- Which relationships to airway, nerves, vessels, or abdominal organs alter functional risk or procedural access? action
Clinical state and complications Represent the lesion's current burden and distinguish baseline disease from acute change.
Baseline burden
Establish the person's usual lesion-related symptoms and limitations.
Functional impact
Record pain, visible or palpable burden, and effects on functions relevant to the anatomical site.
- How does the lesion affect breathing, swallowing, vision, movement, or abdominal function where relevant? measurement
- Which symptoms are attributed to this lesion, and what evidence separates them from unrelated conditions? boundary
Acute change
Capture new swelling and suspected complications as time-stamped episodes.
Swelling episode and escalation
Record the onset and associated findings of an acute episode, including uncertainty between hemorrhage, infection, inflammation, or another cause.
- When did swelling change, and what associated pain, fever, skin change, or imaging evidence was documented? measurement
- Does the episode meet the treating team's escalation criteria for airway compromise or another threatened function? action
Presentation and associated disease Place the lesion in its developmental and wider clinical context without absorbing neighboring disease models.
Presentation history
Separate first detection from inferred onset and document the circumstances of recognition.
Detection versus onset
Preserve prenatal, childhood, or adult detection history and the evidence supporting any claim about earlier existence.
- Was the lesion first identified prenatally, through symptoms, incidentally on imaging, or during surgery? provenance
- What evidence establishes onset rather than merely the date of first recognition? boundary
Associated anomalies
Identify findings that may require links to combined vascular, overgrowth, or complex lymphatic models.
Isolated or associated lesion
Record accompanying abnormalities and specialist conclusions without inferring a syndrome or molecular cause from the lesion name.
- Are there additional vascular components, regional overgrowth, or distant lymphatic abnormalities that challenge an isolated-lesion interpretation? boundary
- If molecular testing was performed, what specimen and result support a lesion-specific or syndromic interpretation? provenance
Management and longitudinal outcome Connect management choices to explicit goals and assess their consequences over time.
Management selection
Capture the specialist's rationale for observation or an intervention.
Goal and option fit
Record the intended benefit and how morphology, extent, symptoms, and adjacent structures affect options considered by the treating team.
- Is the immediate goal surveillance, symptom relief, protection of function, or reduction of lesion burden? action
- What case-specific evidence supports observation, sclerotherapy, surgery, or specialist-directed medical treatment? action
Response and surveillance
Compare follow-up against a documented baseline and distinguish different forms of persistent or returning disease.
Durable benefit and residual lesion
Track functional and imaging outcomes separately, including adverse effects and whether a later finding represents residual disease, recurrence, or temporary swelling.
- What changed in symptoms, function, and measured lesion burden over a specified interval? measurement
- What evidence distinguishes residual lesion from recurrence, and what finding triggers reassessment under the follow-up plan? action
Evidence and external alignment What the world already says about this thing, gathered so the model can be checked against it.
Reported evidence
Findings from the breadth pass, kept separate from the structural claims.
Check these first
Recalled without web access and unsourced; every item is a lead to verify.
- Which of these check these first hold for the sense of cystic lymphangioma this model covers, and on what evidence? provenance
Kinds and varieties
Recalled without web access and unsourced; every item is a lead to verify.
- Which of these kinds and varieties hold for the sense of cystic lymphangioma this model covers, and on what evidence? provenance
Identifiers and schemes
Recalled without web access and unsourced; every item is a lead to verify.
- Which of these identifiers and schemes hold for the sense of cystic lymphangioma this model covers, and on what evidence? provenance
Standards and regulation
Recalled without web access and unsourced; every item is a lead to verify.
- Which of these standards and regulation hold for the sense of cystic lymphangioma this model covers, and on what evidence? provenance
Real-world use
Recalled without web access and unsourced; every item is a lead to verify.
- Which of these real-world use hold for the sense of cystic lymphangioma this model covers, and on what evidence? provenance
Failure modes and hazards
Recalled without web access and unsourced; every item is a lead to verify.
- Which of these failure modes and hazards hold for the sense of cystic lymphangioma this model covers, and on what evidence? provenance
Neighbouring kinds and how to tell them apart
Recalled without web access and unsourced; every item is a lead to verify.
- Which of these neighbouring kinds and how to tell them apart hold for the sense of cystic lymphangioma this model covers, and on what evidence? provenance
Classifiers Filled
- Family
- Thing Registry
- Category
- Information and virtual systems
- Entry kind
- thing
- Plane
- INF
- Domain
- INF.KNW
- Other names and narrower kinds
- congenital cystic hygroma, abdominal cystic lymphangioma, cystic hygroma lethal cleft palate
What it is Filled
Cystic lymphangioma is a historical term for a benign lymphatic malformation composed of dilated, fluid-filled lymphatic spaces, usually corresponding to a macrocystic lymphatic malformation in modern vascular-anomaly terminology.
In scope
- Original diagnostic label, supporting evidence, and mapping to current lymphatic-malformation terminology
- Cyst architecture, anatomical extent, and relationships to vulnerable structures
- Symptoms, functional impairment, and acute complications attributable to the lesion
- Diagnostic uncertainty and distinctions from other cystic or vascular lesions
- Lesion-specific management decisions, response, residual disease, and recurrence
Out of scope
- The full classification of vascular anomalies and all lymphatic malformations
- Independent models of venous malformations, vascular tumors, and nonlymphatic cystic masses
- Whole-person management of associated overgrowth syndromes or complex lymphatic anomalies
- Prenatal chromosomal conditions and screening findings without an established corresponding lesion
- Detailed procedural protocols, medication dosing, and autonomous treatment prescribing
Why it exists Filled
Enable an agent to recognize a lesion recorded as cystic lymphangioma, characterize its extent and clinical state, and support evidence-based specialist assessment and follow-up.
Distinguishing features Filled
- Determine whether the historical label denotes a lymphatic malformation rather than a vascular tumor; ISSVA treats lymphangioma as historical terminology for lymphatic malformation. [ISSVA glossary](https://www.issva.org/UserFiles/file/ISSVAGLOSSARY_UpdatedFullVersion_03152025_Submission_copyright.pdf)
- Document actual cyst architecture before assigning macrocystic, microcystic, or mixed morphology; the word cystic alone does not establish a subtype, and ISSVA does not define a universal precise dividing threshold. [ISSVA glossary](https://www.issva.org/UserFiles/file/ISSVAGLOSSARY_UpdatedFullVersion_03152025_Submission_copyright.pdf)
- Compare enhancement of septa and cyst contents when distinguishing a macrocystic lymphatic lesion from a venous malformation; preserve the interpreting clinician's conclusion rather than treating one imaging feature as definitive. [French national care protocol](https://pmc.ncbi.nlm.nih.gov/articles/PMC9837920/)
- Require a location-specific differential for a cystic mass; an unexplained solid component or discordant clinical course should remain an unresolved diagnostic finding.
- Distinguish a localized lesion from manifestations of a combined malformation or complex lymphatic disorder before extending this entry to systemic disease.
What robots and AI may and may not do Filled
Must not
- Diagnose a lump in a child as a lymphatic malformation without a clinician.
- Advise draining or treating a swelling at home.
- Share images of a child's condition without the parents' consent.
- Use outdated terms in a way that confuses patients about their diagnosis.
Only with a human decision
- Any decision about surgery or sclerotherapy.
May
- Describe lymphatic malformations and the historical term from medical sources.
- Point families to specialist vascular anomaly centres.
Moral aspects Filled
- Visible malformations in children's faces and necks can bring stigma and staring.
- Families need clear information about a benign but sometimes serious condition.
Who is affected
- Children with malformations
- Parents and carers
Owners Filled
Steward
Nobody owns the condition; the treating specialist answers for each patient's care.
Links to other meta-models Filled
parent
- Q1640492 - registry parent class
- Q5201213 - registry parent class
What else AI and robots need to interact with it Filled
Identity and identifiers required Filled
- Vercy registry: vr.tr.cystic-lymphangioma
- Wikidata: Q459896 (https://www.wikidata.org/wiki/Q459896)
Direct properties not applicable Not applicable
- Diagnostic terminology and confidence: Original label; proposed current classification; suspected, supported, confirmed, or disputed; evidence basis
- Anatomical distribution: Body site, laterality, tissue compartments, and continuity between involved regions
- Cyst architecture: Macrocystic, microcystic, mixed, or indeterminate; classification convention recorded
- Lesion and cyst dimensions: Lesion dimensions and representative cyst diameters in mm; volume in mL when measured; modality and date
- Internal imaging characteristics: Septations, fluid characteristics, Doppler findings, enhancement distribution, and any solid component
- Critical-structure involvement: Displacement, compression, encasement, or uncertain relationship to airway, nerves, vessels, bowel, or other site-specific structures
- Current clinical activity: Stable, enlarging, acutely swollen, improving, or indeterminate; observation interval
- Complication and functional burden: Pain, suspected infection, hemorrhage, leakage, and site-specific functional impairment; severity and attribution
- Management and response: Observation or documented intervention; symptom and imaging response; adverse effects; residual or recurrent lesion
Plane INF: no invented physical properties.
Recognition optional Filled
- A soft, painless swelling under the skin, often in the neck or armpit of a young child.
Capabilities and actions required Filled
- Reconcile a historical diagnosis with current terminology while retaining the original report and uncertainty.
- Assemble a lesion map from imaging and clinical assessments, including vulnerable adjacent structures.
- Flag documented acute swelling or functional compromise for clinician review under an established escalation plan.
- Prepare a specialist review summary comparing observation and intervention against lesion-specific goals and constraints.
- Track symptoms and imaging over time, distinguishing residual disease, recurrence, and transient changes.
Hazards and failure modes required Filled
- Large malformations in the neck can press on the airway.
- Infection or bleeding into cysts can cause sudden swelling.
Standards and interfaces required Filled
- The Classification of Vascular Anomalies, issued by the International Society for the Study of Vascular Anomalies, classifies lymphatic malformations and distinguishes macrocystic, microcystic, and mixed forms.
Context of use required Filled
- Cystic lymphangioma appears in clinical records, imaging reports, and pathology descriptions of lymphatic malformations.
- The term is encountered particularly in pediatric care and vascular anomaly services when assessing lesion extent, symptoms, and effects on nearby structures.
- Modern documentation relates the historical label to the lesion's cyst pattern and current lymphatic malformation terminology.
Sources Filled
- Wikidata item Q459896: cystic lymphangioma - identity and sense of the item
- Wikipedia: Cystic hygroma - general description of the item
Open questions
- Does the registry intend cystic lymphangioma to mean predominantly macrocystic lymphatic malformation, or a broader historical category that includes mixed lesions?
- Does an existing Vercy world model already own this concept, requiring this registry entry to link to that publication?
- Which morphology convention should the model adopt while preserving comparability across reports that use different cyst-size thresholds?
- How should prenatal uses of cystic hygroma map to this entry without conflating distinct screening findings and established lesions?
- Which site- and age-specific outcome measures and follow-up criteria have sufficient evidence to standardize across instances?
Machine files
Provenance
thing registry research (pass 2) · unreviewed
Built from: models/things/publications/thing-q459896/spec.json