← Back to catalogue
Research draft

vasculitis

vr.tr.vasculitis · INF.KNW

Let an agent explain vasculitis and its classification, relay causes, symptoms, diagnosis and general treatment from rheumatology sources, describe the forms the registry aliases name, and distinguish vasculitis from atherosclerosis, thrombosis and vasculopathy, routing people to clinicians.

Thing Registry Information and virtual systems

Research draft, second pass

A second pass drafted this model: the structure a model of this thing needs, and what is known about it in the world. The line under this one says how the second half was obtained - researched against sources, or recalled without web access, in which case nothing here was read anywhere and every claim is a lead to verify. Unreviewed either way.

written by Claude from model knowledge without web access - no source was read, every claim is a lead to verify

Researched by: Claude

Purpose and description

Let an agent explain vasculitis and its classification, relay causes, symptoms, diagnosis and general treatment from rheumatology sources, describe the forms the registry aliases name, and distinguish vasculitis from atherosclerosis, thrombosis and vasculopathy, routing people to clinicians.

Inflammation of blood vessel walls, which can narrow, block or weaken vessels and damage organs, classified by vessel size in the Chapel Hill nomenclature into large, medium and small vessel vasculitis, including ANCA-associated vasculitis such as granulomatosis with polyangiitis, central nervous system vasculitis, livedoid vasculitis of the skin and autoimmune vasculitides, with microvasculitis affecting the smallest vessels and the Shwartzman phenomenon, an experimental and clinical reaction causing vascular injury. Treatment typically involves immunosuppression under specialist care. The model routes people to clinicians.

What it is for: Not applicable; a group of diseases.

It can be explain classification; relay diagnosis and treatment; route to clinicians; distinguish related conditions.

Distinguishing features

Vessel wall inflammation

Classified by vessel size

Primary or secondary

Immunosuppressive treatment

What it looks like

Not a visible object; sometimes skin rashes or purpura.

Physical character

classification: Chapel Hill Consensus Conference, 2012 note

giant cell arteritis: most common primary vasculitis in older adults note

ANCA: anti-neutrophil cytoplasmic antibodies note

How it is recognised

Inflammation of blood vessel walls

ANCA-associated, CNS, livedoid, autoimmune vasculitis, microvasculitis, Shwartzman phenomenon

Atherosclerosis is plaque; thrombosis is clotting; vasculopathy is broader vessel disease

Related models

is a kind of - in registry terms

vascular disease

is classified by -

Chapel Hill Consensus Conference

includes -

granulomatosis with polyangiitis

is contrasted with -

atherosclerosis

In practice

Families and kinds

large vessel vasculitis such as giant cell and Takayasu arteritis

medium vessel vasculitis such as polyarteritis nodosa and Kawasaki disease

small vessel ANCA-associated vasculitis

immune complex vasculitis such as IgA vasculitis

single-organ vasculitis such as CNS vasculitis

livedoid vasculopathy and related skin forms

Identifiers

ICD-10 M31 other necrotizing vasculopathies

MeSH D014657 Vasculitis

Standards and regulation

EULAR and ACR guidelines

Chapel Hill nomenclature

Failure modes and hazards

Agents giving personal medical advice

Delayed diagnosis causing organ damage

Registry aliases mixing diseases and experimental phenomena

Also called

anti-neutrophil cytoplasmic antibody-associated vasculitiscentral nervous system vasculitisLivedoid vasculitisShwartzman phenomenonmicrovasculitisautoimmune vasculitishereditary inflammatory vasculitisAdenosine deaminase 2 deficiencypredominantly large-vessel vasculitispredominantly medium-vessel vasculitissecondary vasculitisGolfer's vasculitisangioneuropathyretinal vasculitispolyarteritis nodosasystemic vasculitisUrticarial vasculitisprimary angiitis of the central nervous systemgranulomatous angiitisimmune complex mediated vasculitisretinal perivasculitisprimary polyarteritis nodosasecondary polyarteritis nodosasystemic polyarteritis nodosaPauci-immune

Where this came from

wikidata · CC0 1.0

Drafted structure

Bundle to layer to finding to question, as the second pass will find it: 4 bundles · 8 layers · 8 findings · 16 questions.

Understand What vasculitis is.

Clinical.

Definition

Definition.

Definition

Definition.

  1. What is vasculitis, and how does it differ from atherosclerosis, thrombosis and vasculopathy? definition
  2. Is the user describing sudden vision loss, stroke signs or coughing blood, which need emergency care, or other symptoms needing a clinician? boundary

Forms

Forms.

Forms

Forms.

  1. What are ANCA-associated, CNS, livedoid and autoimmune vasculitis, microvasculitis and the Shwartzman phenomenon? definition
  2. Which entry fits the specific form? action
Medicine Classification and causes.

Clinical.

Classification

Classification.

Classification

Classification.

  1. How does the Chapel Hill nomenclature classify vasculitis by vessel size? provenance
  2. Which references are standard? provenance

Causes

Causes.

Causes

Causes.

  1. What causes primary and secondary vasculitis, including infections, drugs and autoimmune disease? provenance
  2. Which sources are cited? provenance
Care Diagnosis and treatment.

Clinical.

Diagnosis

Diagnosis.

Diagnosis

Diagnosis.

  1. How is vasculitis diagnosed with blood tests, imaging and biopsy, in general terms? provenance
  2. Which entry fits ANCA test? action

Treatment

Treatment.

Treatment

Treatment.

  1. What general treatment approaches do guidelines describe? provenance
  2. Which entry fits immunosuppressive drug? action
Context Living and research.

Context.

Living

Living with vasculitis.

Living

Living.

  1. What support do patient organisations provide? provenance
  2. Which entry fits Vasculitis Foundation or similar? action

Research

Research.

Research

Research.

  1. What is being researched, and what is the Shwartzman phenomenon s role in understanding vascular injury? provenance
  2. Which entry fits Shwartzman phenomenon? action

What the second pass must settle

  • Should ANCA-associated vasculitis and CNS vasculitis be separate primary entries?
  • How should rheumatology sources be linked?
  • The registry entry has merged aliases naming distinct diseases and the Shwartzman phenomenon; should they be split off?